U.S. Department of Health & Human Services Divider Arrow National Institutes of Health Divider Arrow NCATS

Approval Year

Substance Class Protein
Created
by admin
on Wed Apr 02 02:46:51 GMT 2025
Edited
by admin
on Wed Apr 02 02:46:51 GMT 2025
Protein Type ENZYME
Protein Sub Type
Sequence Origin HUMAN
Sequence Type COMPLETE
Record UNII
QK6ZKF2EPJ
Record Status Validated (UNII)
Record Version
  • Download
Name Type Language
ACID CERAMIDASE
Common Name English
PLEXCERASE
Preferred Name English
HSD33
Common Name English
RECOMBINANT HUMAN ACID CERAMIDASE
Common Name English
PHP32
Common Name English
ACYLSPHINGOSINE DEACYLASE
Common Name English
PUTATIVE 32 KDA HEART PROTEIN
Common Name English
ACDASE
Common Name English
N-ACYLSPHINGOSINE AMIDOHYDROLASE
Common Name English
RVT-801
Code English
ASAH1
Common Name English
RHAC
Common Name English
ACID CDASE
Common Name English
Classification Tree Code System Code
EU-Orphan Drug EU/3/15/1536
Created by admin on Wed Apr 02 02:46:51 GMT 2025 , Edited by admin on Wed Apr 02 02:46:51 GMT 2025
FDA ORPHAN DRUG 415313
Created by admin on Wed Apr 02 02:46:51 GMT 2025 , Edited by admin on Wed Apr 02 02:46:51 GMT 2025
Code System Code Type Description
WIKIPEDIA
ASAH1
Created by admin on Wed Apr 02 02:46:51 GMT 2025 , Edited by admin on Wed Apr 02 02:46:51 GMT 2025
PRIMARY
SMS_ID
100000179771
Created by admin on Wed Apr 02 02:46:51 GMT 2025 , Edited by admin on Wed Apr 02 02:46:51 GMT 2025
PRIMARY
FDA UNII
QK6ZKF2EPJ
Created by admin on Wed Apr 02 02:46:51 GMT 2025 , Edited by admin on Wed Apr 02 02:46:51 GMT 2025
PRIMARY
Glycosylation Type HUMAN
Glycosylation Link Type Site
N 2_31
N 2_53
N 2_117
N 2_144
N 2_200
N 2_206
Related Record Type Details
ACTIVE MOIETY
Name Property Type Amount Referenced Substance Defining Parameters References
MOL_WEIGHT CHEMICAL
Molecular Formula CHEMICAL