U.S. Department of Health & Human Services Divider Arrow National Institutes of Health Divider Arrow NCATS

Approval Year

Substance Class Protein
Created
by admin
on Sat Dec 16 14:53:06 UTC 2023
Edited
by admin
on Sat Dec 16 14:53:06 UTC 2023
Protein Type MONOCLONAL ANTIBODY FUSION PROTEIN
Protein Sub Type GLUCOSIDASE|IGG1
Sequence Origin HUMAN
Sequence Type COMPLETE
Record UNII
I6M9Q08XBP
Record Status Validated (UNII)
Record Version
  • Download
Name Type Language
CLERVONAFUSP ALFA
USAN   INN  
Official Name English
VAL1221
Code English
IMMUNOGLOBULIN G1, (HUMANIZED MONOCLONAL 3E10 .GAMMA.1-CHAIN FAB FRAGMENT) FUSION PROTEIN WITH 67-952-LYSOSOMAL .ALPHA.-GLUCOSIDASE (HUMAN RECOMBINANT), DISULFIDE WITH HUMANIZED MONOCLONAL 3E10 .KAPPA.-CHAIN
Common Name English
CLERVONAFUSP ALFA [USAN]
Common Name English
clervonafusp alfa [INN]
Common Name English
IMMUNOGLOBULIN G1-KAPPA, CELL-PENETRATING HUMANIZED FAB FRAGMENT TARGETING THE EQUILIBRATIVE NUCLEOSIDE TRANSPORTER 2 (ENT2), FUSED WITH A HUMAN LYSOSOMAL .ALPHA.-GLUCOSIDASE FRAGMENT, GLYCOFORM ALFA
Common Name English
IMMUNOGLOBULIN G1-KAPPA, CELL-PENETRATING HUMANIZED FAB FRAGMENT TARGETING THE EQUILIBRATIVE NUCLEOSIDE TRANSPORTER 2 (DELAYED-EARLY RESPONSE PROTEIN 12SOLUTE CARRIER FAMILY 29 MEMBER 2) FUSED WITH HUMAN LYSOSOMAL ALPHA-GLUCOSIDASE (ACID MALTASEAGLUCOSID
Common Name English
VAL-1221
Code English
Classification Tree Code System Code
FDA ORPHAN DRUG 651518
Created by admin on Sat Dec 16 14:53:06 UTC 2023 , Edited by admin on Sat Dec 16 14:53:06 UTC 2023
Code System Code Type Description
INN
10973
Created by admin on Sat Dec 16 14:53:06 UTC 2023 , Edited by admin on Sat Dec 16 14:53:06 UTC 2023
PRIMARY
USAN
HI-62
Created by admin on Sat Dec 16 14:53:06 UTC 2023 , Edited by admin on Sat Dec 16 14:53:06 UTC 2023
PRIMARY
CAS
2145123-44-8
Created by admin on Sat Dec 16 14:53:06 UTC 2023 , Edited by admin on Sat Dec 16 14:53:06 UTC 2023
PRIMARY
FDA UNII
I6M9Q08XBP
Created by admin on Sat Dec 16 14:53:06 UTC 2023 , Edited by admin on Sat Dec 16 14:53:06 UTC 2023
PRIMARY
NCI_THESAURUS
C169858
Created by admin on Sat Dec 16 14:53:06 UTC 2023 , Edited by admin on Sat Dec 16 14:53:06 UTC 2023
PRIMARY
From To
1_219 2_218
2_138 2_198
2_23 2_92
1_1109 1_1123
1_818 1_829
1_704 1_729
1_274 1_298
1_263 1_279
1_253 1_280
1_143 1_199
1_22 1_96
Glycosylation Type MAMMALIAN
Glycosylation Link Type Site
N 1_311
N 1_404
N 1_561
N 1_641
N 1_823
N 1_1053
N 1_1096
Related Record Type Details
TARGET->ENZYME REPLACEMENT
Related Record Type Details
ACTIVE MOIETY
Name Property Type Amount Referenced Substance Defining Parameters References
Molecular Formula CHEMICAL
MOL_WEIGHT:NUMBER(CALCULATED) CHEMICAL