Approval Year
Substance Class |
Protein
Created
by
admin
on
Edited
Mon Mar 31 23:18:31 GMT 2025
by
admin
on
Mon Mar 31 23:18:31 GMT 2025
|
Protein Type | ENZYME |
Protein Sub Type | GLYCOSIDASE |
Sequence Origin | HUMAN |
Sequence Type | COMPLETE |
Record UNII |
EO144CP0X9
|
Record Status |
Validated (UNII)
|
Record Version |
|
-
Download
Related Record | Type |
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Name | Type | Language | ||
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Preferred Name | English | ||
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Official Name | English | ||
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Common Name | English | ||
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Common Name | English | ||
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Code | English | ||
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Common Name | English | ||
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Common Name | English | ||
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Common Name | English | ||
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Common Name | English | ||
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Common Name | English |
Classification Tree | Code System | Code | ||
---|---|---|---|---|
|
FDA ORPHAN DRUG |
411913
Created by
admin on Mon Mar 31 23:18:31 GMT 2025 , Edited by admin on Mon Mar 31 23:18:31 GMT 2025
|
Code System | Code | Type | Description | ||
---|---|---|---|---|---|
|
C169795
Created by
admin on Mon Mar 31 23:18:31 GMT 2025 , Edited by admin on Mon Mar 31 23:18:31 GMT 2025
|
PRIMARY | |||
|
P10253
Created by
admin on Mon Mar 31 23:18:31 GMT 2025 , Edited by admin on Mon Mar 31 23:18:31 GMT 2025
|
PRIMARY | |||
|
1802558-87-7
Created by
admin on Mon Mar 31 23:18:31 GMT 2025 , Edited by admin on Mon Mar 31 23:18:31 GMT 2025
|
PRIMARY | |||
|
100000177430
Created by
admin on Mon Mar 31 23:18:31 GMT 2025 , Edited by admin on Mon Mar 31 23:18:31 GMT 2025
|
PRIMARY | |||
|
2565814
Created by
admin on Mon Mar 31 23:18:31 GMT 2025 , Edited by admin on Mon Mar 31 23:18:31 GMT 2025
|
PRIMARY | |||
|
EO144CP0X9
Created by
admin on Mon Mar 31 23:18:31 GMT 2025 , Edited by admin on Mon Mar 31 23:18:31 GMT 2025
|
PRIMARY | |||
|
EO144CP0X9
Created by
admin on Mon Mar 31 23:18:31 GMT 2025 , Edited by admin on Mon Mar 31 23:18:31 GMT 2025
|
PRIMARY | |||
|
HI-22
Created by
admin on Mon Mar 31 23:18:31 GMT 2025 , Edited by admin on Mon Mar 31 23:18:31 GMT 2025
|
PRIMARY | |||
|
Avalglucosidase alfa
Created by
admin on Mon Mar 31 23:18:31 GMT 2025 , Edited by admin on Mon Mar 31 23:18:31 GMT 2025
|
PRIMARY | |||
|
10416
Created by
admin on Mon Mar 31 23:18:31 GMT 2025 , Edited by admin on Mon Mar 31 23:18:31 GMT 2025
|
PRIMARY |
From | To |
---|---|
1_26 | 1_53 |
1_36 | 1_52 |
1_47 | 1_71 |
1_477 | 1_502 |
1_591 | 1_602 |
1_882 | 1_896 |
Glycosylation Type | MAMMALIAN |
Glycosylation Link Type | Site |
---|---|
N | 1_71 |
N | 1_177 |
N | 1_334 |
N | 1_414 |
N | 1_826 |
N | 1_869 |
Related Record | Type | Details | ||
---|---|---|---|---|
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TARGET->ENZYME REPLACEMENT |
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|
SUB_CONCEPT->SUBSTANCE |
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Related Record | Type | Details | ||
---|---|---|---|---|
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ACTIVE MOIETY |
Agent Modifications
Modification Process | Modification Role | Modification Type | Amount | Fragment Name | Fragment ID |
---|---|---|---|---|---|
OXIDIZES SUGAR | OXIDIZING AGENT |
|
SODIUM METAPERIODATE | 98W4A29X43 | |
MANNOSE 6-PHOSPHATE ADDITION TO GLYCOFORM | GLYCOCONJUGATION | CONJUGATING AGENT | 4-((O-6-O-PHOSPHONO-D-MANNO-D-MANNO-D-MANNO-6-O-PHOSPHONO-D-MANNO-D-MANNO-D-MANNO)OXY)BUTANOIC ACID 2-(2-(AMINOOXY)ACETYL)HYDRAZIDE | DJ2K5G8Q34 |
Structural Modifications
Modification Type | Location Site | Location Type | Residue Modified | Extent | Fragment Name | Fragment Approval |
---|---|---|---|---|---|---|
AMINO_ACID_SUBSTITUTION | RESIDUE_SPECIFIC | M |
Amount:
|
METHIONINE SULFOXIDE | XN1XVI4B2C | |
FRAGMENT | RESIDUE_SPECIFIC |
Amount:
|
UNSPECIFIED SUBSTANCE |
c390c2f0
(not in database)
|
Name | Property Type | Amount | Referenced Substance | Defining | Parameters | References |
---|---|---|---|---|---|---|
MOL_WEIGHT:RELATIVE MOLECULAR WEIGHT(GEL ELECTROPHORESIS) | CHEMICAL |
|
||||
Molecular Formula | CHEMICAL |
|