Approval Year
| Substance Class |
Protein
Created
by
admin
on
Edited
Mon Mar 31 23:18:31 GMT 2025
by
admin
on
Mon Mar 31 23:18:31 GMT 2025
|
| Protein Type | ENZYME |
| Protein Sub Type | GLYCOSIDASE |
| Sequence Origin | HUMAN |
| Sequence Type | COMPLETE |
| Record UNII |
EO144CP0X9
|
| Record Status |
Validated (UNII)
|
| Record Version |
|
-
Download
| Related Record | Type |
|---|
| Name | Type | Language | ||
|---|---|---|---|---|
|
Preferred Name | English | ||
|
Official Name | English | ||
|
Common Name | English | ||
|
Common Name | English | ||
|
Code | English | ||
|
Common Name | English | ||
|
Common Name | English | ||
|
Common Name | English | ||
|
Common Name | English | ||
|
Common Name | English |
| Classification Tree | Code System | Code | ||
|---|---|---|---|---|
|
FDA ORPHAN DRUG |
411913
Created by
admin on Mon Mar 31 23:18:31 GMT 2025 , Edited by admin on Mon Mar 31 23:18:31 GMT 2025
|
| Code System | Code | Type | Description | ||
|---|---|---|---|---|---|
|
C169795
Created by
admin on Mon Mar 31 23:18:31 GMT 2025 , Edited by admin on Mon Mar 31 23:18:31 GMT 2025
|
PRIMARY | |||
|
P10253
Created by
admin on Mon Mar 31 23:18:31 GMT 2025 , Edited by admin on Mon Mar 31 23:18:31 GMT 2025
|
PRIMARY | |||
|
1802558-87-7
Created by
admin on Mon Mar 31 23:18:31 GMT 2025 , Edited by admin on Mon Mar 31 23:18:31 GMT 2025
|
PRIMARY | |||
|
100000177430
Created by
admin on Mon Mar 31 23:18:31 GMT 2025 , Edited by admin on Mon Mar 31 23:18:31 GMT 2025
|
PRIMARY | |||
|
2565814
Created by
admin on Mon Mar 31 23:18:31 GMT 2025 , Edited by admin on Mon Mar 31 23:18:31 GMT 2025
|
PRIMARY | |||
|
EO144CP0X9
Created by
admin on Mon Mar 31 23:18:31 GMT 2025 , Edited by admin on Mon Mar 31 23:18:31 GMT 2025
|
PRIMARY | |||
|
EO144CP0X9
Created by
admin on Mon Mar 31 23:18:31 GMT 2025 , Edited by admin on Mon Mar 31 23:18:31 GMT 2025
|
PRIMARY | |||
|
HI-22
Created by
admin on Mon Mar 31 23:18:31 GMT 2025 , Edited by admin on Mon Mar 31 23:18:31 GMT 2025
|
PRIMARY | |||
|
Avalglucosidase alfa
Created by
admin on Mon Mar 31 23:18:31 GMT 2025 , Edited by admin on Mon Mar 31 23:18:31 GMT 2025
|
PRIMARY | |||
|
10416
Created by
admin on Mon Mar 31 23:18:31 GMT 2025 , Edited by admin on Mon Mar 31 23:18:31 GMT 2025
|
PRIMARY |
| From | To |
|---|---|
| 1_26 | 1_53 |
| 1_36 | 1_52 |
| 1_47 | 1_71 |
| 1_477 | 1_502 |
| 1_591 | 1_602 |
| 1_882 | 1_896 |
| Glycosylation Type | MAMMALIAN |
| Glycosylation Link Type | Site |
|---|---|
| N | 1_71 |
| N | 1_177 |
| N | 1_334 |
| N | 1_414 |
| N | 1_826 |
| N | 1_869 |
| Related Record | Type | Details | ||
|---|---|---|---|---|
|
TARGET->ENZYME REPLACEMENT |
|
||
|
SUB_CONCEPT->SUBSTANCE |
|
| Related Record | Type | Details | ||
|---|---|---|---|---|
|
|
ACTIVE MOIETY |
Agent Modifications
| Modification Process | Modification Role | Modification Type | Amount | Fragment Name | Fragment ID |
|---|---|---|---|---|---|
| OXIDIZES SUGAR | OXIDIZING AGENT |
|
SODIUM METAPERIODATE | 98W4A29X43 | |
| MANNOSE 6-PHOSPHATE ADDITION TO GLYCOFORM | GLYCOCONJUGATION | CONJUGATING AGENT | 4-((O-6-O-PHOSPHONO-D-MANNO-D-MANNO-D-MANNO-6-O-PHOSPHONO-D-MANNO-D-MANNO-D-MANNO)OXY)BUTANOIC ACID 2-(2-(AMINOOXY)ACETYL)HYDRAZIDE | DJ2K5G8Q34 |
Structural Modifications
| Modification Type | Location Site | Location Type | Residue Modified | Extent | Fragment Name | Fragment Approval |
|---|---|---|---|---|---|---|
| AMINO_ACID_SUBSTITUTION | RESIDUE_SPECIFIC | M |
Amount:
|
METHIONINE SULFOXIDE | XN1XVI4B2C | |
| FRAGMENT | RESIDUE_SPECIFIC |
Amount:
|
UNSPECIFIED SUBSTANCE |
c390c2f0
(not in database)
|
| Name | Property Type | Amount | Referenced Substance | Defining | Parameters | References |
|---|---|---|---|---|---|---|
| MOL_WEIGHT:RELATIVE MOLECULAR WEIGHT(GEL ELECTROPHORESIS) | CHEMICAL |
|
||||
| Molecular Formula | CHEMICAL |
|