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Approval Year

Substance Class Protein
Created
by admin
on Mon Mar 31 23:18:31 GMT 2025
Edited
by admin
on Mon Mar 31 23:18:31 GMT 2025
Protein Type ENZYME
Protein Sub Type GLYCOSIDASE
Sequence Origin HUMAN
Sequence Type COMPLETE
Record UNII
EO144CP0X9
Record Status Validated (UNII)
Record Version
  • Download
Related Record Type
Name Type Language
GZ-402666
Preferred Name English
AVALGLUCOSIDASE ALFA
USAN   INN  
Official Name English
AVALGLUCOSIDASE ALFA [JAN]
Common Name English
NEOGAA
Common Name English
GZ402666
Code English
AVALGLUCOSIDASE ALFA [USAN]
Common Name English
avalglucosidase alfa [INN]
Common Name English
NEO-RECOMBINANT HUMAN ACID ALPHA-GLUCOSIDASE
Common Name English
Avalglucosidase alfa [WHO-DD]
Common Name English
RECOMBINANT HUMAN ACID .ALPHA.-GLUCOSIDASE
Common Name English
Classification Tree Code System Code
FDA ORPHAN DRUG 411913
Created by admin on Mon Mar 31 23:18:31 GMT 2025 , Edited by admin on Mon Mar 31 23:18:31 GMT 2025
Code System Code Type Description
NCI_THESAURUS
C169795
Created by admin on Mon Mar 31 23:18:31 GMT 2025 , Edited by admin on Mon Mar 31 23:18:31 GMT 2025
PRIMARY
UNIPROT
P10253
Created by admin on Mon Mar 31 23:18:31 GMT 2025 , Edited by admin on Mon Mar 31 23:18:31 GMT 2025
PRIMARY
CAS
1802558-87-7
Created by admin on Mon Mar 31 23:18:31 GMT 2025 , Edited by admin on Mon Mar 31 23:18:31 GMT 2025
PRIMARY
SMS_ID
100000177430
Created by admin on Mon Mar 31 23:18:31 GMT 2025 , Edited by admin on Mon Mar 31 23:18:31 GMT 2025
PRIMARY
RXCUI
2565814
Created by admin on Mon Mar 31 23:18:31 GMT 2025 , Edited by admin on Mon Mar 31 23:18:31 GMT 2025
PRIMARY
DAILYMED
EO144CP0X9
Created by admin on Mon Mar 31 23:18:31 GMT 2025 , Edited by admin on Mon Mar 31 23:18:31 GMT 2025
PRIMARY
FDA UNII
EO144CP0X9
Created by admin on Mon Mar 31 23:18:31 GMT 2025 , Edited by admin on Mon Mar 31 23:18:31 GMT 2025
PRIMARY
USAN
HI-22
Created by admin on Mon Mar 31 23:18:31 GMT 2025 , Edited by admin on Mon Mar 31 23:18:31 GMT 2025
PRIMARY
WIKIPEDIA
Avalglucosidase alfa
Created by admin on Mon Mar 31 23:18:31 GMT 2025 , Edited by admin on Mon Mar 31 23:18:31 GMT 2025
PRIMARY
INN
10416
Created by admin on Mon Mar 31 23:18:31 GMT 2025 , Edited by admin on Mon Mar 31 23:18:31 GMT 2025
PRIMARY
From To
1_26 1_53
1_36 1_52
1_47 1_71
1_477 1_502
1_591 1_602
1_882 1_896
Glycosylation Type MAMMALIAN
Glycosylation Link Type Site
N 1_71
N 1_177
N 1_334
N 1_414
N 1_826
N 1_869
Related Record Type Details
TARGET->ENZYME REPLACEMENT
SUB_CONCEPT->SUBSTANCE
Related Record Type Details
ACTIVE MOIETY

Agent Modifications

Modification Process Modification Role Modification Type Amount Fragment Name Fragment ID
OXIDIZES SUGAR OXIDIZING AGENT SODIUM METAPERIODATE 98W4A29X43
MANNOSE 6-PHOSPHATE ADDITION TO GLYCOFORM GLYCOCONJUGATION CONJUGATING AGENT 4-((O-6-O-PHOSPHONO-D-MANNO-D-MANNO-D-MANNO-6-O-PHOSPHONO-D-MANNO-D-MANNO-D-MANNO)OXY)BUTANOIC ACID 2-(2-(AMINOOXY)ACETYL)HYDRAZIDE DJ2K5G8Q34

Structural Modifications

Modification Type Location Site Location Type Residue Modified Extent Fragment Name Fragment Approval
AMINO_ACID_SUBSTITUTION RESIDUE_SPECIFIC M Amount: METHIONINE SULFOXIDE XN1XVI4B2C
FRAGMENT RESIDUE_SPECIFIC Amount: UNSPECIFIED SUBSTANCE
c390c2f0
(not in database)
Name Property Type Amount Referenced Substance Defining Parameters References
MOL_WEIGHT:RELATIVE MOLECULAR WEIGHT(GEL ELECTROPHORESIS) CHEMICAL
Molecular Formula CHEMICAL