U.S. Department of Health & Human Services Divider Arrow National Institutes of Health Divider Arrow NCATS

Approval Year

Substance Class Protein
Created
by admin
on Tue Apr 01 21:47:33 GMT 2025
Edited
by admin
on Tue Apr 01 21:47:33 GMT 2025
Protein Type ENZYME
Protein Sub Type SULFOHYDROLASE
Sequence Origin HUMAN
Sequence Type COMPLETE
Record UNII
ZS87P77DQC
Record Status Validated (UNII)
Record Version
  • Download
Name Type Language
SOBI003
Preferred Name English
SOBI-003
Code English
CHEMICALLY MODIFIED RECOMBINANT SULFAMIDASE
Common Name English
Classification Tree Code System Code
FDA ORPHAN DRUG 583617
Created by admin on Tue Apr 01 21:47:33 GMT 2025 , Edited by admin on Tue Apr 01 21:47:33 GMT 2025
Code System Code Type Description
FDA UNII
ZS87P77DQC
Created by admin on Tue Apr 01 21:47:33 GMT 2025 , Edited by admin on Tue Apr 01 21:47:33 GMT 2025
PRIMARY
SMS_ID
300000011221
Created by admin on Tue Apr 01 21:47:33 GMT 2025 , Edited by admin on Tue Apr 01 21:47:33 GMT 2025
PRIMARY
DRUG BANK
DB15451
Created by admin on Tue Apr 01 21:47:33 GMT 2025 , Edited by admin on Tue Apr 01 21:47:33 GMT 2025
PRIMARY
From To
1_461 1_475
1_163 1_174
Glycosylation Type MAMMALIAN
Glycosylation Link Type Site
N 1_21
N 1_122
N 1_131
N 1_244
N 1_393

Agent Modifications

Modification Process Modification Role Modification Type Amount Fragment Name Fragment ID
OXIDATION OXIDIZES SUGAR OXIDIZING AGENT SODIUM METAPERIODATE 98W4A29X43
HYDROGENATION REDUCE END GROUPS HYDROGENATION Sodium borohydride 87L0B9CPPA

Structural Modifications

Modification Type Location Site Location Type Residue Modified Extent Fragment Name Fragment Approval
AMINO_ACID_SUBSTITUTION [1_50] SITE_SPECIFIC 3-OXO-ALANINE 3LXS1M9IE5
Name Property Type Amount Referenced Substance Defining Parameters References
Molecular Formula CHEMICAL
MOL_WEIGHT:NUMBER(CALCULATED) CHEMICAL