Approval Year
| Substance Class |
Protein
Created
by
admin
on
Edited
Mon Mar 31 21:37:23 GMT 2025
by
admin
on
Mon Mar 31 21:37:23 GMT 2025
|
| Protein Type | ENZYME |
| Protein Sub Type | SULFOHYDROLASE |
| Sequence Origin | HUMAN |
| Sequence Type | COMPLETE |
| Record UNII |
X0MD128U01
|
| Record Status |
Validated (UNII)
|
| Record Version |
|
-
Download
| Name | Type | Language | ||
|---|---|---|---|---|
|
Common Name | English | ||
|
Preferred Name | English | ||
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Common Name | English | ||
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Common Name | English | ||
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Common Name | English | ||
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Common Name | English | ||
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Common Name | English | ||
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Common Name | English | ||
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Common Name | English | ||
|
Code | English | ||
|
Common Name | English |
| Classification Tree | Code System | Code | ||
|---|---|---|---|---|
|
FDA ORPHAN DRUG |
258408
Created by
admin on Mon Mar 31 21:37:23 GMT 2025 , Edited by admin on Mon Mar 31 21:37:23 GMT 2025
|
| Code System | Code | Type | Description | ||
|---|---|---|---|---|---|
|
X0MD128U01
Created by
admin on Mon Mar 31 21:37:23 GMT 2025 , Edited by admin on Mon Mar 31 21:37:23 GMT 2025
|
PRIMARY | |||
|
DB12722
Created by
admin on Mon Mar 31 21:37:23 GMT 2025 , Edited by admin on Mon Mar 31 21:37:23 GMT 2025
|
PRIMARY | |||
|
P51688
Created by
admin on Mon Mar 31 21:37:23 GMT 2025 , Edited by admin on Mon Mar 31 21:37:23 GMT 2025
|
PRIMARY | |||
|
300000010661
Created by
admin on Mon Mar 31 21:37:23 GMT 2025 , Edited by admin on Mon Mar 31 21:37:23 GMT 2025
|
PRIMARY |
| From | To |
|---|---|
| 1_163 | 1_174 |
| 1_461 | 1_475 |
| Glycosylation Type | HUMAN |
| Glycosylation Link Type | Site |
|---|---|
| N | 1_21 |
| N | 1_122 |
| N | 1_131 |
| N | 1_244 |
| N | 1_393 |
| Related Record | Type | Details | ||
|---|---|---|---|---|
|
VECTOR->EXPRESSED PROTEIN |
|
||
|
ENZYME REPLACEMENT->TARGET |
|
Structural Modifications
| Modification Type | Location Site | Location Type | Residue Modified | Extent | Fragment Name | Fragment Approval |
|---|---|---|---|---|---|---|
| AMINO_ACID_SUBSTITUTION | [1_50] | SITE_SPECIFIC |
Amount:
|
3-OXO-ALANINE | 3LXS1M9IE5 |
| Name | Property Type | Amount | Referenced Substance | Defining | Parameters | References |
|---|---|---|---|---|---|---|
| MOL_WEIGHT | CHEMICAL |
|
||||
| Molecular Formula | CHEMICAL |
|