U.S. Department of Health & Human Services Divider Arrow National Institutes of Health Divider Arrow NCATS

Approval Year

Substance Class Protein
Created
by admin
on Mon Mar 31 21:37:23 GMT 2025
Edited
by admin
on Mon Mar 31 21:37:23 GMT 2025
Protein Type ENZYME
Protein Sub Type SULFOHYDROLASE
Sequence Origin HUMAN
Sequence Type COMPLETE
Record UNII
X0MD128U01
Record Status Validated (UNII)
Record Version
  • Download
Name Type Language
N-SULFOGLUCOSAMINE SULFOHYDROLASE
Common Name English
N-SULFOGLUCOSAMINE SULFOHYDROLASE RECOMBINANT
Preferred Name English
AMIDASE, SULFOGLUCOSAMINE SULF-
Common Name English
SHP-610
Common Name English
Recombinant human heparan N-sulfatase
Common Name English
SULFAMIDASE RECOMBINANT
Common Name English
N-SULPHOGLUCOSAMINE SULPHOHYDROLASE
Common Name English
N-SULFOGLUCOSAMINE SULFOHYDROLASE HUMAN
Common Name English
SULPHAMIDASE
Common Name English
HGT-1410
Code English
SULFOGLUCOSAMINE SULFAMIDASE
Common Name English
Classification Tree Code System Code
FDA ORPHAN DRUG 258408
Created by admin on Mon Mar 31 21:37:23 GMT 2025 , Edited by admin on Mon Mar 31 21:37:23 GMT 2025
Code System Code Type Description
FDA UNII
X0MD128U01
Created by admin on Mon Mar 31 21:37:23 GMT 2025 , Edited by admin on Mon Mar 31 21:37:23 GMT 2025
PRIMARY
DRUG BANK
DB12722
Created by admin on Mon Mar 31 21:37:23 GMT 2025 , Edited by admin on Mon Mar 31 21:37:23 GMT 2025
PRIMARY
UNIPROT
P51688
Created by admin on Mon Mar 31 21:37:23 GMT 2025 , Edited by admin on Mon Mar 31 21:37:23 GMT 2025
PRIMARY
SMS_ID
300000010661
Created by admin on Mon Mar 31 21:37:23 GMT 2025 , Edited by admin on Mon Mar 31 21:37:23 GMT 2025
PRIMARY
From To
1_163 1_174
1_461 1_475
Glycosylation Type HUMAN
Glycosylation Link Type Site
N 1_21
N 1_122
N 1_131
N 1_244
N 1_393
Related Record Type Details
VECTOR->EXPRESSED PROTEIN
ENZYME REPLACEMENT->TARGET

Structural Modifications

Modification Type Location Site Location Type Residue Modified Extent Fragment Name Fragment Approval
AMINO_ACID_SUBSTITUTION [1_50] SITE_SPECIFIC Amount: 3-OXO-ALANINE 3LXS1M9IE5
Name Property Type Amount Referenced Substance Defining Parameters References
MOL_WEIGHT CHEMICAL
Molecular Formula CHEMICAL