U.S. Department of Health & Human Services Divider Arrow National Institutes of Health Divider Arrow NCATS

Approval Year

Substance Class Protein
Created
by admin
on Wed Apr 02 01:58:47 GMT 2025
Edited
by admin
on Wed Apr 02 01:58:47 GMT 2025
Protein Sub Type
Sequence Type COMPLETE
Record UNII
TNF61X6TFD
Record Status Validated (UNII)
Record Version
  • Download
Name Type Language
(3-METHYL-2-OXOBUTANOATE DEHYDROGENASE (LIPOAMIDE)) KINASE, MITOCHONDRIAL
Common Name English
BCKD-KINASE
Preferred Name English
BCKDK
Common Name English
BRANCHED-CHAIN ALPHA-KETOACID DEHYDROGENASE KINASE
Common Name English
BCKDHKIN
Common Name English
Code System Code Type Description
PHAROS
O14874
Created by admin on Wed Apr 02 01:58:47 GMT 2025 , Edited by admin on Wed Apr 02 01:58:47 GMT 2025
PRIMARY
FDA UNII
TNF61X6TFD
Created by admin on Wed Apr 02 01:58:47 GMT 2025 , Edited by admin on Wed Apr 02 01:58:47 GMT 2025
PRIMARY
UNIPROT
O14874
Created by admin on Wed Apr 02 01:58:47 GMT 2025 , Edited by admin on Wed Apr 02 01:58:47 GMT 2025
PRIMARY
Related Record Type Details
INHIBITOR -> TARGET
IC50

Structural Modifications

Modification Type Location Site Location Type Residue Modified Extent Fragment Name Fragment Approval
AMINO ACID SUBSTITUTION [1_1] [1_22] [1_326] [1_330] S DEXFOSFOSERINE VI4F0K069V
AMINO ACID SUBSTITUTION [1_162] [1_203] K N6-ACETYLLYSINE 470AD5VY1X
Name Property Type Amount Referenced Substance Defining Parameters References
MOL_WEIGHT CHEMICAL
Molecular Formula CHEMICAL