U.S. Department of Health & Human Services Divider Arrow National Institutes of Health Divider Arrow NCATS

Approval Year

Substance Class Protein
Created
by admin
on Wed Apr 02 08:50:29 GMT 2025
Edited
by admin
on Wed Apr 02 08:50:29 GMT 2025
Protein Sub Type
Record UNII
T9O2IHM7K4
Record Status Validated (UNII)
Record Version
  • Download
Name Type Language
5-AMINOLEVULINATE SYNTHASE, NONSPECIFIC, MITOCHONDRIAL
Common Name English
ALAS1
Preferred Name English
Code System Code Type Description
FDA UNII
T9O2IHM7K4
Created by admin on Wed Apr 02 08:50:29 GMT 2025 , Edited by admin on Wed Apr 02 08:50:29 GMT 2025
PRIMARY
UNIPROT
P13196
Created by admin on Wed Apr 02 08:50:29 GMT 2025 , Edited by admin on Wed Apr 02 08:50:29 GMT 2025
PRIMARY
Related Record Type Details
INHIBITOR OF EXPRESSION->TARGET
Results in downregulation of ALAS1 mRNA and prevents accumulation of neurotoxic ?-aminolevulinic acid and porphobilinogen levels that are associated with acute porphyria attacks.
Name Property Type Amount Referenced Substance Defining Parameters References
MOL_WEIGHT:NUMBER(CALCULATED) CHEMICAL