U.S. Department of Health & Human Services Divider Arrow National Institutes of Health Divider Arrow NCATS

Approval Year

Substance Class Protein
Created
by admin
on Sat Dec 16 15:41:45 GMT 2023
Edited
by admin
on Sat Dec 16 15:41:45 GMT 2023
Protein Type FC FUSION PROTEIN
Protein Sub Type IGG1
Sequence Origin HUMAN
Sequence Type COMPLETE
Record UNII
QLD7UJN8CF
Record Status Validated (UNII)
Record Version
  • Download
Name Type Language
Tividenofusp Alfa
INN  
Official Name English
DNL-310, RECOMBINANT IDURONATE 2-SULFATASE
Common Name English
ENZYME TRANSPORT VEHICLE SPECIFIC FOR THE TRANSFERRIN RECEPTOR FUSED TO IDURONATE 2-SULFATASE
Common Name English
ETV:IDS
Common Name English
human iduronate 2-sulfatase (IDS, α- L-iduronate sulfate sulfatase, EC:3.1.6.13) pro-protein (1-525), fused via the peptide linker 526 GGGGS 530 to a human immunoglobulin G1 C-terminal Fc fragment (531-757) variant (L 544>A, L 545>A, T 676>S, L 678>A, Y
Common Name English
DNL-310
Code English
Iduronate-2-sulfatase (human) fusion protein with immunoglobulin Fcab, anti-(human type 1 transferrin receptor) (synthetic human γ1-chain 2), (536→6′),(539→9′)-bis(disulfide) with immunoglobulin Fcab anti-(human type 1 transferrin receptor) (syn
Common Name English
DNL310
Code English
tividenofusp alfa [INN]
Common Name English
Classification Tree Code System Code
FDA ORPHAN DRUG 671118
Created by admin on Sat Dec 16 15:41:45 GMT 2023 , Edited by admin on Sat Dec 16 15:41:45 GMT 2023
Code System Code Type Description
CAS
2641020-57-5
Created by admin on Sat Dec 16 15:41:45 GMT 2023 , Edited by admin on Sat Dec 16 15:41:45 GMT 2023
PRIMARY
FDA UNII
QLD7UJN8CF
Created by admin on Sat Dec 16 15:41:45 GMT 2023 , Edited by admin on Sat Dec 16 15:41:45 GMT 2023
PRIMARY
INN
12197
Created by admin on Sat Dec 16 15:41:45 GMT 2023 , Edited by admin on Sat Dec 16 15:41:45 GMT 2023
PRIMARY
NCI_THESAURUS
C199121
Created by admin on Sat Dec 16 15:41:45 GMT 2023 , Edited by admin on Sat Dec 16 15:41:45 GMT 2023
PRIMARY
From To
1_536 2_6
1_539 2_9
1_146 1_159
1_397 1_407
1_571 1_631
1_677 1_735
2_41 2_101
2_147 2_205
Glycosylation Type MAMMALIAN
Glycosylation Link Type Site
N 1_90
N 1_221
N 1_255
N 1_300
N 1_488
N 1_512
N 1_607
N 2_77
Related Record Type Details
ACTIVE MOIETY
enzyme replacement therapy for iduronate 2-sulfatase, Treatment of mucopolysaccharidosis type II
Name Property Type Amount Referenced Substance Defining Parameters References
MOL_WEIGHT:NUMBER(CALCULATED) CHEMICAL
Molecular Formula CHEMICAL