U.S. Department of Health & Human Services Divider Arrow National Institutes of Health Divider Arrow NCATS

Approval Year

Substance Class Structurally Diverse
Created
by admin
on Wed Apr 02 10:00:38 GMT 2025
Edited
by admin
on Wed Apr 02 10:00:38 GMT 2025
Source Materials Class ORGANISM
Source Materials Type RECOMBINANT VIRUS
Source Materials State LIVE SELF-COMPLEMENTARY NON-REPLICATING GENETICALLY MODIFIED
Organism Family Parvoviridae
Organism Genus Dependoparvovirus
Organism Species adeno-associated dependoparvovirus a
Author NONE
Infraspecific Type SUBSTRAIN
Infraspecific Name scAAVrh74.MHCK7.hSGCB
Part whole
Record UNII
NM4FH5S2OW
Record Status Validated (UNII)
Record Version
  • Download
Name Type Language
BIDRIDISTROGENE XEBOPARVOVEC
INN  
Official Name English
SRP-9003
Preferred Name English
DNA (RECOMBINANT SELF-COMPLEMENTARY ADENO-ASSOCIATED VIRUS AAVRH74 VECTOR SRP-9003 MHCK7 PROMOTER PLUS HUMAN .BETA.-SARCOGLYCAN-SPECIFYING)
Common Name English
SCAAVRH74.MHCK7.HSGCB
Common Name English
bidridistrogene xeboparvovec [INN]
Common Name English
Code System Code Type Description
CAS
2365142-14-7
Created by admin on Wed Apr 02 10:00:38 GMT 2025 , Edited by admin on Wed Apr 02 10:00:38 GMT 2025
PRIMARY
NCI_THESAURUS
C188604
Created by admin on Wed Apr 02 10:00:38 GMT 2025 , Edited by admin on Wed Apr 02 10:00:38 GMT 2025
PRIMARY
SMS_ID
300000015960
Created by admin on Wed Apr 02 10:00:38 GMT 2025 , Edited by admin on Wed Apr 02 10:00:38 GMT 2025
PRIMARY
INN
11619
Created by admin on Wed Apr 02 10:00:38 GMT 2025 , Edited by admin on Wed Apr 02 10:00:38 GMT 2025
PRIMARY
FDA UNII
NM4FH5S2OW
Created by admin on Wed Apr 02 10:00:38 GMT 2025 , Edited by admin on Wed Apr 02 10:00:38 GMT 2025
PRIMARY
Related Record Type Details
EXPRESSED PROTEIN->VECTOR
Related Record Type Details
ACTIVE MOIETY
LGMD2E patients

Structural Modifications

Modification Type Location Site Location Type Residue Modified Extent Fragment Name Fragment Approval
TRANSGENE UNSPECIFIED SUBSTANCE
2883a2b5
(not in database)