U.S. Department of Health & Human Services Divider Arrow National Institutes of Health Divider Arrow NCATS

Approval Year

Substance Class Protein
Created
by admin
on Wed Apr 02 00:26:40 GMT 2025
Edited
by admin
on Wed Apr 02 00:26:40 GMT 2025
Protein Type ENZYME
Protein Sub Type
Sequence Origin HUMAN
Sequence Type COMPLETE
Record UNII
HNX0Q31MDU
Record Status Validated (UNII)
Record Version
  • Download
Name Type Language
ORNITHINE CARBAMOYLTRANSFERASE, MITOCHONDRIAL
Common Name English
HUMAN ORNITHINE TRANSCARBAMYLASE
Preferred Name English
ORNITHINE TRANSCARBAMYLASE
Common Name English
Code System Code Type Description
FDA UNII
HNX0Q31MDU
Created by admin on Wed Apr 02 00:26:40 GMT 2025 , Edited by admin on Wed Apr 02 00:26:40 GMT 2025
PRIMARY
UNIPROT
P00480
Created by admin on Wed Apr 02 00:26:40 GMT 2025 , Edited by admin on Wed Apr 02 00:26:40 GMT 2025
PRIMARY
Related Record Type Details
ENZYME REPLACEMENT->TARGET
VECTOR->EXPRESSED PROTEIN

Structural Modifications

Modification Type Location Site Location Type Residue Modified Extent Fragment Name Fragment Approval
AMINO_ACID_SUBSTITUTION [1_38] [1_56] [1_112] [1_189] [1_199] [1_206] [1_211] [1_260] [1_275] [2_38] [2_56] [2_112] [2_189] [2_199] [2_206] [2_211] [2_260] [2_275] [3_38] [3_56] [3_112] [3_189] [3_199] [3_206] [3_211] [3_260] [3_275] SITE_SPECIFIC N6-ACETYLLYSINE 470AD5VY1X
AMINO_ACID_SUBSTITUTION [1_101] [2_101] [3_101] SITE_SPECIFIC DEXFOSFOSERINE VI4F0K069V
AMINO_ACID_SUBSTITUTION [1_48] [1_242] [2_48] [2_242] [3_48] [3_242] SITE_SPECIFIC N6-SUCCINYLLYSINE 3LH35AJA5L
Name Property Type Amount Referenced Substance Defining Parameters References
MOL_WEIGHT:NUMBER(CALCULATED) CHEMICAL