U.S. Department of Health & Human Services Divider Arrow National Institutes of Health Divider Arrow NCATS

Approval Year

Substance Class Protein
Created
by admin
on Mon Mar 31 22:56:59 GMT 2025
Edited
by admin
on Mon Mar 31 22:56:59 GMT 2025
Protein Sub Type
Sequence Type COMPLETE
Record UNII
5GCF8EPY6R
Record Status Validated (UNII)
Record Version
  • Download
Name Type Language
IDURSULFASE BETA
INN   WHO-DD  
INN  
Official Name English
HUNTERASE
Preferred Name English
Idursulfase beta [WHO-DD]
Common Name English
idursulfase beta [INN]
Common Name English
IDURONATE 2-SULFATASE (A-L-IDURONATE SULFATE SULFATASE), HUMAN PROENZYME PRODUCED IN CHO CELLS (GLYCOFORM BETA)
Common Name English
IDURSULFASE BETA [JAN]
Common Name English
IDURSULFASE .BETA.
Common Name English
Classification Tree Code System Code
WHO-ATC A16AB16
Created by admin on Mon Mar 31 22:56:59 GMT 2025 , Edited by admin on Mon Mar 31 22:56:59 GMT 2025
FDA ORPHAN DRUG 385712
Created by admin on Mon Mar 31 22:56:59 GMT 2025 , Edited by admin on Mon Mar 31 22:56:59 GMT 2025
Code System Code Type Description
FDA UNII
5GCF8EPY6R
Created by admin on Mon Mar 31 22:56:59 GMT 2025 , Edited by admin on Mon Mar 31 22:56:59 GMT 2025
PRIMARY
SMS_ID
100000178235
Created by admin on Mon Mar 31 22:56:59 GMT 2025 , Edited by admin on Mon Mar 31 22:56:59 GMT 2025
PRIMARY
INN
9504
Created by admin on Mon Mar 31 22:56:59 GMT 2025 , Edited by admin on Mon Mar 31 22:56:59 GMT 2025
PRIMARY
CAS
1271734-34-9
Created by admin on Mon Mar 31 22:56:59 GMT 2025 , Edited by admin on Mon Mar 31 22:56:59 GMT 2025
PRIMARY
NCI_THESAURUS
C166846
Created by admin on Mon Mar 31 22:56:59 GMT 2025 , Edited by admin on Mon Mar 31 22:56:59 GMT 2025
PRIMARY
From To
1_146 1_159
1_397 1_407
Glycosylation Type HUMAN
Glycosylation Link Type Site
N 1_6
N 1_90
N 1_119
N 1_221
N 1_225
N 1_300
N 1_488
N 1_512
Related Record Type Details
ACTIVE MOIETY

Structural Modifications

Modification Type Location Site Location Type Residue Modified Extent Fragment Name Fragment Approval
AMINO_ACID_SUBSTITUTION [1_59] Ala 3-OXO-ALANINE 3LXS1M9IE5
Name Property Type Amount Referenced Substance Defining Parameters References
Molecular Formula CHEMICAL
MOL_WEIGHT:NUMBER(CALCULATED) CHEMICAL