Details
| Stereochemistry | ACHIRAL |
| Molecular Formula | C6H10O4 |
| Molecular Weight | 146.1412 |
| Optical Activity | NONE |
| Defined Stereocenters | 0 / 0 |
| E/Z Centers | 0 |
| Charge | 0 |
SHOW SMILES / InChI
SMILES
CC(CC(O)=O)CC(O)=O
InChI
InChIKey=XJMMNTGIMDZPMU-UHFFFAOYSA-N
InChI=1S/C6H10O4/c1-4(2-5(7)8)3-6(9)10/h4H,2-3H2,1H3,(H,7,8)(H,9,10)
| Molecular Formula | C6H10O4 |
| Molecular Weight | 146.1412 |
| Charge | 0 |
| Count |
|
| Stereochemistry | ACHIRAL |
| Additional Stereochemistry | No |
| Defined Stereocenters | 0 / 0 |
| E/Z Centers | 0 |
| Optical Activity | NONE |
Approval Year
PubMed
| Title | Date | PubMed |
|---|---|---|
| OPA3, mutated in 3-methylglutaconic aciduria type III, encodes two transcripts targeted primarily to mitochondria. | 2010-06 |
|
| Striatum is more vulnerable to oxidative damage induced by the metabolites accumulating in 3-hydroxy-3-methylglutaryl-CoA lyase deficiency as compared to liver. | 2009-06 |
|
| Inherited mitochondrial optic neuropathies. | 2009-03 |
|
| Costeff optic atrophy syndrome: new clinical case and novel molecular findings. | 2008-12 |
|
| Induction of oxidative stress by the metabolites accumulating in 3-methylglutaconic aciduria in cerebral cortex of young rats. | 2008-03-12 |
|
| 3-methylglutaconic aciduria type 4 manifesting as Leigh syndrome in 2 siblings. | 2007-02 |
|
| 3-Methylglutaric acid as a 13C solid-state NMR standard. | 2006-10 |
|
| NMR spectroscopic studies on the late onset form of 3-methylglutaconic aciduria type I and other defects in leucine metabolism. | 2006-04 |
|
| A new sensitive isotropic-anisotropic separation experiment-SPEED MAS. | 2004-06 |
|
| Vitamin E analogues as inducers of apoptosis: structure-function relation. | 2003-06-16 |
|
| 3-methyglutaconic aciduria in a Chinese patient with glycogen storage disease Ib. | 2003 |
|
| 3-Methylglutaconic aciduria type III in a non-Iraqi-Jewish kindred: clinical and molecular findings. | 2002-07 |
|
| Type III 3-methylglutaconic aciduria (optic atrophy plus syndrome, or Costeff optic atrophy syndrome): identification of the OPA3 gene and its founder mutation in Iraqi Jews. | 2001-12 |
|
| 3-Hydroxy-3-methylglutaric aciduria in an Italian patient is caused by a new nonsense mutation in the HMGCL gene. | 2001-07 |
|
| Mitochondrial DNA depletion associated with partial complex II and IV deficiencies and 3-methylglutaconic aciduria. | 2001-02 |
|
| Age-related reference values for urinary organic acids in a healthy Turkish pediatric population. | 1994-06 |
|
| Behr's syndrome and 3-methylglutaconic aciduria. | 1992-10-15 |
|
| Inherited 3-methylglutaconic aciduria in two brothers--another defect of leucine metabolism. | 1982-10 |
|
| Studies on a child suspected of having a dficiency in 3-hydroxy-3-methylglutaryl-Co A lyase. | 1979-07-02 |
Patents
| Substance Class |
Chemical
Created
by
admin
on
Edited
Mon Mar 31 19:18:01 GMT 2025
by
admin
on
Mon Mar 31 19:18:01 GMT 2025
|
| Record UNII |
3Q0P190C7B
|
| Record Status |
Validated (UNII)
|
| Record Version |
|
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14870
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DTXSID50211649
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68566
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626-51-7
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210-951-5
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12284
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3Q0P190C7B
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C033686
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