U.S. Department of Health & Human Services Divider Arrow National Institutes of Health Divider Arrow NCATS

Details

Stereochemistry ABSOLUTE
Molecular Formula C7H14N2O4S
Molecular Weight 222.262
Optical Activity UNSPECIFIED
Defined Stereocenters 2 / 2
E/Z Centers 0
Charge 0

SHOW SMILES / InChI
Structure of CYSTATHIONINE, L-

SMILES

N[C@@H](CCSC[C@H](N)C(O)=O)C(O)=O

InChI

InChIKey=ILRYLPWNYFXEMH-WHFBIAKZSA-N
InChI=1S/C7H14N2O4S/c8-4(6(10)11)1-2-14-3-5(9)7(12)13/h4-5H,1-3,8-9H2,(H,10,11)(H,12,13)/t4-,5-/m0/s1

HIDE SMILES / InChI

Molecular Formula C7H14N2O4S
Molecular Weight 222.262
Charge 0
Count
Stereochemistry ABSOLUTE
Additional Stereochemistry No
Defined Stereocenters 2 / 2
E/Z Centers 0
Optical Activity UNSPECIFIED

Approval Year

PubMed

PubMed

TitleDatePubMed
Alterations in hepatic metabolism of sulfur amino acids in non-obese type-2 diabetic Goto-Kakizaki rats.
2013-07-05
New insights into the metabolism of organomercury compounds: mercury-containing cysteine S-conjugates are substrates of human glutamine transaminase K and potent inactivators of cystathionine γ-lyase.
2012-01-01
Metabolic biomarkers of increased oxidative stress and impaired methylation capacity in children with autism.
2004-12
The three-dimensional structure of cystathionine beta-lyase from Arabidopsis and its substrate specificity.
2001-06
Role of homocysteine, cystathionine and methylmalonic acid measurement for diagnosis of vitamin deficiency in high-aged subjects.
2000-12
Cystathionine beta-synthase mutations in homocystinuria.
1999
Elevation of serum cystathionine levels in patients with cobalamin and folate deficiency.
1993-06-15
Automated screening of urine samples for carbohydrates, organic and amino acids after treatment with urease.
1991-01-02
Cystathionine disappearance with neuronal loss: a possible neuronal marker.
1985-08
Similarity of the oxidation products of L-cystathionine by L-amino acid oxidase to those excreted by cystathioninuric patients.
1983-09-10
Megaloblastic anemia as a result of an abnormal transcobalamin II (Cardeza).
1979-11
Free amino acids and related substances in human glial tumours and in fetal brain: comparison with normal adult brain.
1976-11-19
A method of determination of cystathionine and its distribution in human brain.
1966-02
Patents
Substance Class Chemical
Created
by admin
on Mon Mar 31 21:19:24 GMT 2025
Edited
by admin
on Mon Mar 31 21:19:24 GMT 2025
Record UNII
375YFJ481O
Record Status Validated (UNII)
Record Version
  • Download
Name Type Language
L-CYSTATHIONINE
MI  
Preferred Name English
CYSTATHIONINE, L-
Systematic Name English
L-HOMOCYSTEINE, S-(2-AMINO-2-CARBOXYETHYL)-, (R)-
Systematic Name English
BUTANOIC ACID, 2-AMINO-4-((2-AMINO-2-CARBOXYETHYL)THIO)-, (R-(R*,S*))-
Common Name English
L-(+)-CYSTATHIONINE
Systematic Name English
L-CYSTATHIONINE [MI]
Common Name English
CYSTATHIONINE
Systematic Name English
Classification Tree Code System Code
LOINC 32236-2
Created by admin on Mon Mar 31 21:19:24 GMT 2025 , Edited by admin on Mon Mar 31 21:19:24 GMT 2025
LOINC 25092-8
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LOINC 26964-7
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LOINC 26607-2
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LOINC 28599-9
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LOINC 13393-4
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LOINC 53069-1
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LOINC 2172-5
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LOINC 6880-9
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LOINC 26592-6
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LOINC 13370-2
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LOINC 2174-1
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LOINC 25388-0
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LOINC 27349-0
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NCI_THESAURUS C73539
Created by admin on Mon Mar 31 21:19:24 GMT 2025 , Edited by admin on Mon Mar 31 21:19:24 GMT 2025
LOINC 13724-0
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LOINC 30070-7
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LOINC 25888-9
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LOINC 16705-6
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LOINC 2173-3
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LOINC 25887-1
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LOINC 53066-7
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Code System Code Type Description
FDA UNII
375YFJ481O
Created by admin on Mon Mar 31 21:19:24 GMT 2025 , Edited by admin on Mon Mar 31 21:19:24 GMT 2025
PRIMARY
WIKIPEDIA
CYSTATHIONINE
Created by admin on Mon Mar 31 21:19:24 GMT 2025 , Edited by admin on Mon Mar 31 21:19:24 GMT 2025
PRIMARY
ECHA (EC/EINECS)
200-295-8
Created by admin on Mon Mar 31 21:19:24 GMT 2025 , Edited by admin on Mon Mar 31 21:19:24 GMT 2025
PRIMARY
CAS
56-88-2
Created by admin on Mon Mar 31 21:19:24 GMT 2025 , Edited by admin on Mon Mar 31 21:19:24 GMT 2025
PRIMARY
MERCK INDEX
m4044
Created by admin on Mon Mar 31 21:19:24 GMT 2025 , Edited by admin on Mon Mar 31 21:19:24 GMT 2025
PRIMARY Merck Index
CHEBI
17755
Created by admin on Mon Mar 31 21:19:24 GMT 2025 , Edited by admin on Mon Mar 31 21:19:24 GMT 2025
PRIMARY
EPA CompTox
DTXSID20971384
Created by admin on Mon Mar 31 21:19:24 GMT 2025 , Edited by admin on Mon Mar 31 21:19:24 GMT 2025
PRIMARY
PUBCHEM
439258
Created by admin on Mon Mar 31 21:19:24 GMT 2025 , Edited by admin on Mon Mar 31 21:19:24 GMT 2025
PRIMARY
CHEBI
17482
Created by admin on Mon Mar 31 21:19:24 GMT 2025 , Edited by admin on Mon Mar 31 21:19:24 GMT 2025
PRIMARY
Related Record Type Details
METABOLITE -> PARENT